A Case Report on Decompensated Chronic Liver Disease with Budd–Chiari Syndrome

ABSTRACT

The rare illness, known as Budd-Chiari Syndrome (BCS), is characterized by hepatic venous outflow tract obstruction and can arise from the right atrium, inferior vena cava, or the tiny hepatic veins within the liver. It is an uncommon liver condition in which obstructions, typically caused by blood clots, restrict the hepatic veins, preventing blood from exiting the liver and returning to the heart. As a result, the liver enlarges (hepatomegaly), accumulates fluid (ascites), and causes abdominal pain. We present a rare case of a young female diagnosed with decompensated chronic liver disease secondary to Budd–Chiari syndrome, who came with the features of abdominal distension and weight loss, along with a Model for end stage liver disease Na score of 20 and splenomegaly with portal hypertension. The diagnosis was confirmed by Doppler ultrasonography and contrast-enhanced CT of the abdomen, supported by abnormal laboratory parameters including prolonged prothrombin time with elevated INR, decreased serum albumin and total protein levels, and elevated WBC count, lymphocytes, GGT, and bilirubin. Management included anticoagulants, antibiotics, statins, proton pump inhibitors, β blockers, hepatoprotective agents, diuretics, and other supportive care, with a step-up approach planned for hepatic venous outflow restoration to prevent disease progression.

KEYWORDS

• Budd-Chairi syndrome
• Ascities
• Hepatomegaly
• Liver
• Endoluminal venous lesion

Showing references and in-text citations exactly as published.

• DOI10.5530/jppcm.20260020Copy

RELATED ARTICLES

Matched on section and article type within this issue of JPPCM.

• Article · VOLUME 12, ISSUE 3Exogenous Cushing’s Syndrome with Steroid-Induced Adrenal Insufficiency Complicated by Sepsis and a Non-healing Diabetic Foot Ulcer: A Case ReportHardik Prajapat, Meharunisha Siddiqui, Daizy Tak, Narendra Bheemraj Parihar, Jishi Joshi Joseph, Mahendra Singh Rathore · pp. 180–183Case ReportSame type: Article
• Article · VOLUME 12, ISSUE 3Concurrent Cryptococcal Meningitis, Disseminated Histoplasmosis, and Tuberculosis Lymphadenitis in a Newly Diagnosed Human Immunodeficiency Virus Patient: An Unusual Case ReportPallavi Kadam, V.H.T. Swamy, Sudheer Areeparambil, Srirama Rao, Ramesh Madhan · pp. 184–187Case ReportSame type: Article
• Article · VOLUME 12, ISSUE 3A Case Report on Cervical Canal Stenosis Secondary to Ossification of Posterior Longitudinal LigamentKorikani Lavanya, Galanki Arundathi Kavya, Shaik Muskan, Kriti Suberi Chettri, Chinta Nageswara Rao · pp. 188–190Case ReportSame type: Article
• Article · VOLUME 12, ISSUE 3A Case Reports On Bilateral Diffuse Cystic Lung Disease (Pulmonary Langerhans’ Cell Histiocytosis)Faizan Ali Shaik, Snehitha Kasu, Kedareswari Jonnadula, Hemalatha Ganjala, Hima Sathwika Manchikanti, Sandhya Kota, Ramya Valaparla · pp. 191–195Case ReportSame type: Article